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IJSTR >> Volume 4 - Issue 1, January 2015 Edition

International Journal of Scientific & Technology Research  
International Journal of Scientific & Technology Research

Website: http://www.ijstr.org

ISSN 2277-8616

Review Of Consultations For Children With Sickle Cell Disease (CHR Kenitra Morocco)

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Mouden Samira, Ahami Ahmad Omar, Mouilly Mustapha, Fayez Noureddine, Hajji Ahmad



Index Terms: Keywords: child, sickle cell crises, Environment, socio-economic determinants region gharb Chrarda benihssen, pediatrics.



Abstract: Also called sickle cell anemia Sickle cell anemia is a genetic disease of autosomal recessive linked to abnormal structure of the hemoglobin which leads to the formation of hemoglobin S (HbS). The descriptive and cross that we conducted at the pediatric ward of the regional hospital Gharb study Chrarda benihessen Kénitra we were enjoying a work force of 164 children with sickle cell disease over a period of twenty four months ( from June 2010 to June 2012 ) . On average seven to eight (7-8) new cases per year. The majority of these children admitted to the exhibit acute complications that are typically associated either to a chronic hemolytic anemia, vaso -occlusive crisis, acute chest syndrome, or severe infections, which aims to identify factors likely to play a role in the occurrence of the sickle cell crises. This can cause severe functional consequences (with renal, lung, bone, etc.). In order to understand the problems and difficulties faced by sickle cell and their families in their daily lives, we have established a protocol form of a questionnaire exploring various aspects related to eating habits and lifestyle of these children. and their families, as well as family socioeconomic status, and the context of environmental life The size of the control group study consists of 60 children aged 7-14 years. Clinical and analytical information is collected from records, medical records and doctors during consultations of these patients. The results show that 71% of these children are from rural areas against 20% of children of urban origin, while 9% live in suburban area however. The majority of parents have irregular income, low educational attainment. 68% of these children use septic false in parallel they use well water in consumption and domestic use. Clinical examination and blood cell abnormalities formula revealed prevalence of 76% for fever cases painful crises severe recurrent and unpredictable also observed, as well as "acute chest syndrome " ( pneumonia or pulmonary infarction), a bone or joint necrosis unpredictable 43% for leukocytosis . As we noted the presence of diarrhea in this sample. In conclusion, the present study showed an association between the frequency of sickle cell crises especially infectious presented by the children studied and the environmental quality of family life in which the child develops.



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